AU - Kohsari, M.R AU - Borhani, M TI - DRASH SYNDROME AND ITS FIRST CASE REPORT IN IRAN PT - JOURNAL ARTICLE TA - gums-med JN - gums-med VO - 5 VI - 16 IP - 16 4099 - http://journal.gums.ac.ir/article-1-1881-en.html 4100 - http://journal.gums.ac.ir/article-1-1881-en.pdf SO - gums-med 16 ABĀ  - ABSTRACT: DRASH Syndrome is a rare congenital disorder,and the triad of drash syndrome are progressive renal insufficiency ,male pseudohermaphroditism & Wilms tumor .All of the reported cases were sporadic and autosomal dominant inheritance was suspected in some references. We diagnosed a 32- month child with this syndrome in IRAN in 1993. He was presented with wilms tumor and also had male pseudohermaphroditism and renal insufficiency. The patient died due to fluid & electrolyte disturbance .His parents had consanguinity marriage and thus there is a possibility of autosomal recessive inheritance. In this patient , the age for onset of nephropathy was higher than that in similar cases. CP - IRAN IN - LG - eng PB - gums-med PG - 47 PT - Research YR - 1996