TY - JOUR JF - gums-med JO - JGUMS VL - 5 IS - 16 PY - 1996 Y1 - 1996/4/01 TI - DRASH SYNDROME AND ITS FIRST CASE REPORT IN IRAN TT - سندرم DRASH و گزارش اولین مورد آن در ایران N2 - ABSTRACT: DRASH Syndrome is a rare congenital disorder,and the triad of drash syndrome are progressive renal insufficiency ,male pseudohermaphroditism & Wilms tumor .All of the reported cases were sporadic and autosomal dominant inheritance was suspected in some references. We diagnosed a 32- month child with this syndrome in IRAN in 1993. He was presented with wilms tumor and also had male pseudohermaphroditism and renal insufficiency. The patient died due to fluid & electrolyte disturbance .His parents had consanguinity marriage and thus there is a possibility of autosomal recessive inheritance. In this patient , the age for onset of nephropathy was higher than that in similar cases. SP - 47 EP - 51 AU - Kohsari, M.R AU - Borhani, M AD - UR - http://journal.gums.ac.ir/article-1-1881-en.html ER -